Resumen
Introduction: Thrombotic thrombocytopenic purpura (TTP) is a rare and highly lethal microangiopathic disorder characterized by microangiopathic hemolytic anemia, thrombocytopenia, and multi-organ involvement associated with neurological, renal, and systemic abnormalities. Objective: Diagnosing this condition is challenging, as treatment should not be delayed and must be initiated as soon as possible. The current gold standard for diagnosis is the presence of decreased ADAMTS-13 levels (<10%). Clinical observation: We present the case of a previously healthy 32-year-old male patient with petechiae and jaundice. Laboratory tests pointed to a diagnosis of thrombotic thrombocytopenic purpura (hemolytic anemia, severe thrombocytopenia, and low ADAMTS-13). He had a poor response to corticosteroids, and fresh frozen plasma was chosen, which proved effective. Conclusion: TTP is a rare hematological emergency.
Citas
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Copyright (c) 2025 Roger Antonio Sernaque Mechato, Percy Cruz Gonzales Morán, Andrea Paola Cruz Pérez
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