Revista de la Facultad de Medicina

Primary cutaneous T-cell lymphoma presenting as a widespread macular dermatosis in a young adult.

DOI: https://doi.org/10.37345/23045329.v4i1.170

Case reports | Publicado: 2026-06-30

Autores:

  • María José Polanco García
  • Vilma Renée García Benítez
  • Alejandra Maria Gonzalez Orellana

Introduction:  Primary Cutaneous T-cell Lymphomas represent the most common subtype of Cutaneous Lymphomas and are characterized by clonal proliferation of skin-homing T lymphocytes. Their clinical presentation is often heterogeneous and may mimic benign inflammatory dermatoses.  Objective:  We report the case of a 21-year-old male presenting with disseminated macular dermatosis associated with pancytopenia.   Results:  Histopathology revealed epidermotropism with atypical lymphocytic infiltration. Immunohistochemistry showed CD3 (+), CD4 (+), CD8 (+), CD5 (+), and CD20 (−), confirming T-cell lineage.  Conclusion:  This case highlights the importance of clinicopathologic correlation in persistent atypical cutaneous lesions in young patients.

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Cómo citar

Primary cutaneous T-cell lymphoma presenting as a widespread macular dermatosis in a young adult. (2026). Revista De La Facultad De Medicina, 4(1). https://doi.org/10.37345/23045329.v4i1.170